Porphyria

Porphyria - term for all types of violations of porphyrin metabolism and its clinical manifestations. To date single classification porfirii not. There are porfirii true, mixed and symptomatic. To the true P. include skin P. [P. congenital (porphyria congenita), late skin P. (see Porphyria cutanea tarda) and melasma] and porphyrin disease (see). Symptomatic, or secondary, P. occur in other diseases and intoxications. In congenital P. porphyrins are formed in the bone marrow (eritropoeticescoe P.). Other forms of porphyria, including porphyrin disease, belong to the group of hepatic P., in which porphyrins are formed in the liver.