Thalassemia

Thalassemia (synonym: Cooley's anemia, anemia milenalena) is a hereditary hemolytic anemia in children. The disease develops in connection with the violation of the synthesis of normal hemoglobin and conservation synthesis fetal (embryonic) of hemoglobin, education degenerative forms and rapid destruction of red blood cells.
In the USSR thalassemia occurs in the republics of Transcaucasia and Central Asia.
There are two main forms of illness: a large thalassemia - homozygous variant at which clinical symptoms are more pronounced, and thalassemia minor is heterozygous option (see Heredity).
Clinically observed progressive hypochromic anemia, eritroblastopenia, enlarged liver and spleen, jaundice color of skin, osteoporosis, deformation of the facial skull, the child is physically underdeveloped.

thalassemia
The blood of a patient suffering from thalassemia. Visible machinewide erythrocytes.

The diagnosis is established on the basis of clinical and hematological data, as well as detecting michelemidnight of erythrocytes with the Central location of hemoglobin (Fig).
Treatment of symptomatic: it is shown transfusion of blood and erythrocyte mass, removal of the spleen. The effect is temporary. The prognosis depends on the form of the disease. People can live up to maturity only at low thalassemia flowing with less severe clinical manifestations. Cm. Anemia (children), Hemolytic anemia, a Hereditary disease.